Notes in ✧ Porphyrias

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Status	Last Update	Fields
Published	01/14/2024	Hemoglobin is made of {{c1::heme}} and {{c1::globin}}
Published	01/14/2024	Heme is composed of {{c1::iron}} and {{c1::protoporphyrin}}
Published	01/14/2024	Congenital sideroblastic anemia is most commonly due to a defect in the enzyme {{c1::δ-aminolevulinic acid synthase (ALAS)}}
Published	01/14/2024	{{c2::Sideroblastic}} anemia may be caused by {{c1::lead}} poisoning
Published	01/14/2024	{{c2::Sideroblastic}} anemia may be caused by vitamin {{c1::B6}} deficiency
Published	01/14/2024	What is the treatment for sideroblastic anemia?{{c1::Pyridoxine (vitamin B6)}}
Published	01/14/2024	Barbiturates are contraindicated in patients with {{c1::porphyrias::hematologic pathology}}
Published	01/14/2024	{{c2::Acute intermittent porphyria}} is due to deficiency of the enzyme {{c1::porphobilinogen deaminase}}
Published	01/14/2024	What is the mode of inheritance of acute intermittent porphyria?{{c1::Autosomal dominant}}
Published	01/14/2024	The symptoms of {{c4::acute intermittent porphyria}} may be remembered with the "5 P's": 1. {{c1::Painful abdomen}}2. {{c2::Port wine-colored urine}}3…
Published	01/14/2024	Does acute intermittent porphyria (AIP) present with photosensitivity?{{c1::No}}
Published	01/14/2024	Treatment for acute intermittent porphyria include {{c1::heme}} and {{c1::glucose}}, which inhibit ALA synthesis
Published	01/14/2024	{{c2::Porphyria cutanea tarda}} is due to deficiency of the enzyme {{c1::uroporphyrinogen decarboxylase}}
Published	01/14/2024	Which porphyrea presents with blistering cutaneous photosensitivity and hyperpigmentation? {{c1::Porphyria cutanea tarda}}
Published	01/14/2024	What is the most common porphyria?{{c1::Porphyria cutanea tarda}}
Published	01/14/2024	Porphyrea cutanea tarda is exacerbated by {{c1::alcohol}} consumption
Published	01/14/2024	Griseofulvin is a(n) {{c1::inducer}} of CYP-450
Published	01/14/2024	Phenobarbital is a(n) {{c1::inducer}} of CYP-450
Published	01/14/2024	The B6 depletion with Isoniazid use can lead to decreased {{c1::protoporphyrin}} synthesis, leading to a(n) {{c1::sideroblastic}} anemia
Published	01/14/2024	Which antifungal is contraindicated in patients with porphyrias?{{c1::Griseofulvin}}
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