Review Note
Last Update: 10/08/2024 02:55 PM
Current Deck: Genes and Development::Week 3::LE024 Platelet Disorders
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{{c1::Glanzmann’s Thrombasthenia (GT)}}
- Presentation: normal platelet morphology
- Platelet aggregometry: impaired ADP & epinephrine response
- Genetics: autosomal recessive defect in GPIIb-IIIa receptor
- Mechanism: reduced receptor affinity to von Willebrand factor
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